Sunday, 24 December 2017

Health News: Fibrous dysplasia



📚📚Fibrous dysplasia is a noninherited developmental anomaly  that causes tissue to be replaced by bone.
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🚑Patients with small, monostotic lesions may be asymptomatic, however, bone pain, swelling, and tenderness are common presentations in symptomatic patients. Endocrine disturbances may be the initial presentation in other patients.
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📒📘Polyostotic  fibrous dysplasia  (involving or relating to many bones ) fibrous dysplasia can occur as a part of McCune-Albright syndrome (unilateral polyostotic fibrous dysplasia, ipsilateral café-au-lait spots on the skin, and endocrine disturbances such as precocious puberty) or Mazabraud syndrome (polyostotic fibrous dysplasia and soft-tissue myxomas).
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📍📌The most common sites of skeletal involvement are the ribs, proximal femur, and craniofacial bones, typically the posterior maxilla. The lesion may involve only a small segment of bone or it may occupy its entire length.
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💊💉Although the manifestations of the polyostotic form may be severe, it does not proliferate and generally becomes  dormant at puberty.
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Emanuel is scheduled to undergo his first lifesaving surgery at Holtz Children's Hospital in January.
IKF Wonderfund, a Jackson Health Foundation program that helps critically ill children from countries around the world gain immediate access to lifesaving or life-changing medical treatments, took Emanuel's case.  
Video by University of Miami

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