🎥: Ectopia Cordis
📚Ectopia cordis is an extremely rare congenital malformation where the heart is located partially or totally outside the thoracic cavity. The four main ectopic positions are:
👉🏽adjacent to the thorax: ~60 %
📚It results from the failure of migration of lateral mesoderm into the midline.
🏨Ectopia cordis may occur as an isolated malformation or it may be associated with a larger category of ventral body wall defects that affect the thorax, abdomen or both.
A well-known association is pentalogy of Cantrell 1 which comprises of:
👉🏽omphalocele (typically supraumbilical)
👉🏽congenital diaphragmatic hernia
👉🏽congenital heart disease